Calcifying odontogenic cyst (COC) is rare benign odontogenic lesion. COC was reported about 0.3–0.8 % from all odontogenic cysts. The lession has a unique characteristic. It has a features of a cyst but also has a similiar features with neoplasm. COC frequently affected the canine area, involved intraosseously or extraosseusly. COC has a simil- iar clinical & radiograph appeareances with another odontogenic cyst and it was challenging for dentist to diagnose without specific examination.The purpose of this paper is to present how important an adequate examination (clin- ical-radiograph and histopatological) to diagnosed and treated COC correctly in order to prevent the recurrences. 21 years old female patient came into clinic with chief complaint an unerupted teeth in the anterior segment of maxilla. An intraoral examination showed a painless buldging& swelling in anterior maxilla with unerupted incicisor teeth and can be felt only by palpation. Orthopantomogram showed an unicyctyc lession involved an unerupted permanent maxillary central incisor.The lesion was removed using surgical excision and the affected tooth was re- moved using odontectomy. Histopathological post-op examination has been taken and the lession was diagnosed as COC. After after 1 months of follow-up, mucosal was healing and no recurrence of the lesion was observed. COC frequently involved an unerupted teeth and it makes COC has similar features with another odontogenic lessions. Clinical,radiograph examination, correct surgical planning and histopatological examination must be taken to pre- vent misdiagnosed and recurrences in order to achieve favorable outcome for the patient.